Double Aortic Arch

Michael P. D'Alessandro, M.D.
Peer Review Status: Internally Peer Reviewed

Etiology/Pathophysiology:
The ascending aorta arises anterior to the trachea and divides into 2 arches which pass posterior and to the right and anterior and to the left of the trachea and esophagus, creating the vascular ring. The right arch gives off the right common carotid and subclavian arteries and the left arch gives off the left common carotid and subclavian arteries.The two arches rejoin posteriorly to form the descending aorta.

There are two types:

• Type 1 has both arches patent and functioning and this type is most common
• Type 2 has both arches intact but one is atretic, usually the left

Pathology:
Not applicable

Imaging Findings:
The posterior right arch is more promient and higher than the left arch. The esophagram on the lateral view shows variable anterior compression of the trachea and a large posterior indentation of the esophagus by the right arch. The esophagram on the AP view shows bilateral compression of the esophagus forming a reverse S sign with the superior curve due to compression from the higher right arch and the inferior curve due to compression from the left arch.

DDX:

• Not applicable

References:

• Correlapedia

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See related Provider Topics Congenital Heart Disease, Genetics/Birth Defects or Heart and Circulation.

See related Patient Topics Congenital Heart Disease, Genetics/Birth Defects or Heart and Circulation.

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